|Table of Contents|

Epithelioid cell tumor（PEComa） of the uterine：A case report and literature review

Journal Of Modern Oncology[ISSN:1672-4992/CN:61-1415/R]

Issue:
2018 01
Page:
106-108
Research Field:
Publishing date:

Info

Title:
Epithelioid cell tumor（PEComa） of the uterine：A case report and literature review
Author(s):
Wu Xiaotong; Wang Ling; Xu Zhihong; Zhang Xiaoxiao; Han Liying
The Second Hospital of Jilin University，Jilin Changchun 130012，China.
Keywords:
uterine tumor; perivascular epithelioid cell tumor(PEComa); literature review
PACS:
R733.33
DOI:
10.3969/j.issn.1672-4992.2018.01.028
Abstract:
Objective：To discussion the perivascular epithelioid cell tumor(PEComa)，pathology and the characteristics of immune performance，diagnosis and antidiastole，treatment and prognoses.Methods：Discussion on a case，received and cured by our hospital in 2016，who was a 66-year-old female patient.The patient admission to hospital because of massive vaginal bleeding.The initial diagnostic was myoma of uterus and then was performed a hysterectomy and a bilateral salpingo-oophorectomy.After the operation，the pathology return was PEComa.Aimming at the material report of the case，review some related literature.Results：In the case，womb PEComa appears in intramural pregnancy，with widely hemorrhagic necrosis and cells' atypia-HMB45(partly-B)，MelanA(+)、SMA(-).Concusion：Perivascular epithelioid cell tumor is a rare mesenchymal tumor.The biological property of the uterine PEComa was undefined.Some materials have reported malignant lesions.The treatment was mainly the complete excision.The efficiency of chemoradiation is indistinctive.Long-term follow-up visit is important.

References:

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Last Update: 2017-11-30