|Table of Contents|

Analysis of clinical features in cholangitis as the main manifestation of langerhans cell histiocytosis

Journal Of Modern Oncology[ISSN:1672-4992/CN:61-1415/R]

Issue:
2017 05
Page:
798-801
Research Field:
Publishing date:

Info

Title:
Analysis of clinical features in cholangitis as the main manifestation of langerhans cell histiocytosis
Author(s):
Yuan Heli1; Ouyang Wenxian2; Zhang Hui2; Tang Lian2; Li Shuangjie2
1.Department of Paediatrics,North China University of Science and Technology,Hebei Tangshan 063000，China;2.Liver center,Hunan Children's Hospital,Hunan Changsha 410007,China.
Keywords:
langerhans cell histiocytosis（LCH）; cholangitis; liver; children
PACS:
R735.8
DOI:
10.3969/j.issn.1672-4992.2017.05.033
Abstract:
Objective：To summarize the clinical characteristics of Langerhans cell organization cell hyperplasia disease (LCH)，especially the cholangitis is the main performance of the cases.Methods： The clinical manifestations，laboratory examination，bone marrow cytology of 12 patients were retrospectively analyzed，and the relevant literature was reviewed.8 patients had single system disease and the Other 6 with multisystem disease.Results： In 12 children with LCH，11 had a different degree of jaundice.8 cases were performed by ultrasound，and 2 cases had failure of skeletal system.6 cases had lung invasion.Conclusion：The diagnosis of LCH is complex and it may involve multiple organ systems，the clinical manifestations and the changes in the process，from an early stage to an isolated performance to later multiple system performance.

References:

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Last Update: 2017-01-26